A case report on retroperitoneal PNET/EWS
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چکیده
Primitive neuroectodermal tumor (PNET) and Ewing’s sarcoma (EWS) are small round cell tumors occurring mainly in children and adolescents, rarely in adults. It can occur in multiple tissues and organs including kidney, adrenal, bladder, liver, small intestine, colon and rectum, with a preferred location within the chest area, in the limbs and around the spine, but with rare cases of abdominal, pelvic or retroperitoneal. Here we present a case of the retroperitoneal PENT/EWS in a 38-year-old man and we discuss the clinical features, histopathological characteristics, diagnosis, treatment and prognosis.
منابع مشابه
Peripheral primitive neuroectodermal tumor of the dura in a 51-year-old woman following intensive treatment for breast cancer
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INTRODUCTION Primitive neuroectodermal tumor (PNET)/Ewing's sarcoma (EWS) belongs to a family of neoplasms that are presumed to originate from the neuroectodermal crest. PNET/EWSs are highly aggressive malignancies that usually present in the form of bone or soft tissue masses and usually affect adolescents and young adults. Primary PNET/EWS of the kidney is very rare. CASE PRESENTATION We pr...
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Objectives: The present study is to report the clinical and pathological features of the primary primitive neuroectodermal tumor, Ewing’s sarcoma (PNET/EWS) of urinary bladder. Methods: A case of PNET/EWS in urinary bladder was reported. The literatures of 14 cases of PNET/EWS were reviewed according to clinical manifestation and pathological characteristics. Results: A 2-year-old boy presented...
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تاریخ انتشار 2013